Table 1 Indications for pediatric living-donor liver transplantation in Japan (n = 2224)

Cholestatic liver disease

1649

74.1

Biliary atresia

1471

66.1

Alagille syndrome

70

3.1

Bayler disease

33

1.5

Others

75

3.4

Metabolic liver disease

194

8.7

Wilson’s disease

59

2.6

Ornithine transcarbamylase deficiency

40

1.8

Carbamoyl phosphate synthetase 1 deficiency

9

0.4

Others

86

3.9

Acute liver failure

192

8.6

Hepatitis B

9

0.4

Drug induced

2

0.1

Auto immune hepatitis

2

0.1

Unknown

163

7.3

Others

16

0.7

Neoplastic disease

66

3.0

Hepatoblastoma

52

2.3

Hepatocellular carcinoma

6

0.3

Others

8

0.4

Vascular disease

32

1.4

Congenital absence of portal vein

21

0.9

Budd-Chiari syndrome

7

0.3

Others

4

0.2

Re-transplantation

76

3.4

2nd transplantation

74

3.3

3rd transplantation

2

0.1

Others

15

0.7

Total

2224

100